Anti-OTC Polyclonal Antibody - SAlexa Fluor 633
Cat: K010426P - SAlexa Fluor 633
Summary:
| 【Product name】：Anti-OTC Polyclonal Antibody - SAlexa Fluor 633 | 【Source】：Rabbit |
| 【Isotype】：IgG | 【Purification】：Affinity purification |
| 【Gene ID】：5009 | 【Swiss Prot】：P00480 |
| 【Tested applications】：IHC,WB | |
| 【Recommended dilution】：WB 1:1000-4000. IHC 1:50-100. | |
| 【Immunogen】：Recombinant protein of human OTC | |
| 【Storage】：Store at -20℃. Avoid freeze / thaw cycles. | |
Background:
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also.
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